Paeds Cases · cardiology
Ventricular septal defect — structured clinical encounter
Structured encounter testing the approach to an infant presenting in overcirculation heart failure from a moderate-to-large ventricular septal defect at six weeks: recognition, the four-to-eight-week pathophysiology, immediate management with doses, and the closure and counselling plan.
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Station brief (candidate)
You are the paediatric registrar in the emergency department. A six-week-old term infant presents with a three-week history of worsening tachypnoea, taking 40 minutes to finish 60 mL of feeds while sweating, and crossing two weight centiles downward. On examination there is a pansystolic murmur at the lower left sternal border, an apical mid-diastolic murmur, a hyperactive precordium, and hepatomegaly. Oxygen saturations are 98 percent in air. The team asks you to establish the diagnosis and immediate management, then proceed to the echocardiogram, the closure plan, and the family counselling. You have 12 minutes with the team and 5 minutes for examiner discussion. [1]
References5ShowHide
- [1]Hoffman JI; Kaplan S The incidence of congenital heart disease. J Am Coll Cardiol, 2002.PMID 12084585
- [4]Butera G; Carminati M; Chessa M; et al Transcatheter closure of perimembranous ventricular septal defects: early and long-term results. J Am Coll Cardiol, 2007.PMID 17868812
- [6]Galiè N; Beghetti M; Gatzoulis MA; Granton J; et al Bosentan therapy in patients with Eisenmenger syndrome: a multicenter, double-blind, randomized, placebo-controlled study. Circulation, 2006.PMID 16801459
- [8]Wilson WR; Gewitz M; Lockhart PB; Bolger AF; et al Prevention of Viridans Group Streptococcal Infective Endocarditis: AHA Scientific Statement. Circulation, 2021.PMID 33853363
- [9]Baumgartner H; De Backer J The ESC Clinical Practice Guidelines for the Management of Adult Congenital Heart Disease. Eur Heart J, 2020.PMID 33128054