Paeds Cases · fetal-neonatal-and-perinatal
Hypoplastic left heart syndrome — antenatal planning structured clinical encounter
Structured encounter testing antenatal planning for a ductal-dependent cardiac lesion: place, time and capability of delivery, prostaglandin readiness, the staged surgical strategy, and capability-matched rural follow-up design.
On this page & tools
Target exams
Station brief (candidate)
You are the paediatric registrar at the antenatal multidisciplinary meeting. Mei is 34 years old at 22 weeks gestation. The fetal echocardiogram confirms hypoplastic left heart syndrome with a normal karyotype and no other anomalies. She lives three hours from the nearest cardiac centre and asks what will happen when the baby is born and whether surgery will be needed. She has two young children and limited leave from work. You have 12 minutes with the patient and 5 minutes for examiner discussion. [1] [2]
You have read the opening of this case. The complete unit — every section and its primary-source references — is part of the Paediatrics Fellowship fellowship atlas.
References4Show ledgerHide ledger
- [1]Donofrio MT, Moon-Grady AJ, Hornberger LK, et al. Diagnosis and treatment of fetal cardiac disease: a scientific statement from the American Heart Association. Circulation, 2014.PMID 24763516
- [2]Benachi A, Sarnacki S. Prenatal counselling and the role of the paediatric surgeon. Seminars in pediatric surgery, 2014.PMID 25459006
- [19]Tulzer A, Huhta JC, Hochpoechler J, et al. Hypoplastic Left Heart Syndrome: Is There a Role for Fetal Therapy? Frontiers in pediatrics, 2022.PMID 35874565
- [20]Martinez-Biarge M, Jowett VC, Cowan FM, et al. Neurodevelopmental outcome in children with congenital heart disease. Seminars in fetal & neonatal medicine, 2013.PMID 23706956