O&G Cases · Antenatal care — haematological disorders
Sickle crisis with acute chest syndrome in pregnancy — emergency management station
Emergency management station on sickle cell crisis with acute chest syndrome in pregnancy. Tests the candidate on the crisis bundle with drug doses, recognition of acute chest syndrome, exchange transfusion thresholds, phenotypic blood matching, and fetal and team communication. Includes assessor key and marking domains.
On this page
Study tools
Target exams
Station brief
Format. Emergency management station, approximately 12 minutes. You are the obstetric registrar in the maternity assessment unit. A midwife, an anaesthetist and a haematology registrar are available on call. The assessor will run the clock and feed you new observations. [1]
Candidate instruction. Lead the management of sickle cell crisis with acute chest syndrome in pregnancy. Verbalise your drug orders with doses, your escalation triggers, your transfusion decisions, and your communication with the patient and team. [1][3]
References6ShowHide
- [1]Oteng-Ntim E, Pavord S, Howard R, et al. Management of sickle cell disease in pregnancy. A British Society for Haematology Guideline Br J Haematol, 2021.PMID 34409598
- [2]Oteng-Ntim E, Meeks D, Seed PT, Webster L, Howard J, Doyle P, Chappell LC Adverse maternal and perinatal outcomes in pregnant women with sickle cell disease: systematic review and meta-analysis Blood, 2015.PMID 25800049
- [3]Chou ST, Alsawas M, Fasano RM, Field JJ, Hendrickson JE, Howard J, Kameka M, Kwiatkowski JL, Pirenne F, Shi PA, Stowell SR, Thein SL, Westhoff CM, Wong TE, Akl EA American Society of Hematology 2020 guidelines for sickle cell disease: transfusion support Blood Adv, 2020.PMID 31985807
- [4]Boulet SL, Okoroh EM, Azonobi I, Grant A, Craig Hooper C Sickle cell disease in pregnancy: maternal complications in a Medicaid-enrolled population Matern Child Health J, 2013.PMID 23315242
- [5]Howard RJ, Lillis C, Tuck SM Contraceptives, counselling, and pregnancy in women with sickle cell disease BMJ, 1993.PMID 8343632
- [6]Taher AT, Iolascon A, Matar CF, Bou-Fakhredin R, de Franceschi L, Cappellini MD, Barcellini W, Russo R, Andolfo I, Tyan P, Gulbis B, Aydinok Y, Anagnou NP, Bencaiova GA, Tamary H, Martinez PA, Forni G, Vindigni R Recommendations for Pregnancy in Rare Inherited Anemias HemaSphere, 2020.PMID 32885142