Clubfoot (Talipes Equinovarus)
Summary
Clubfoot (congenital talipes equinovarus, CTEV) is a congenital foot deformity affecting 1 in 1,000 live births, making it one of the most common musculoskeletal birth defects. The deformity involves four components remembered by the mnemonic CAVE: Cavus, Adductus, Varus, and Equinus. The Ponseti method of serial casting and percutaneous Achilles tenotomy has revolutionised treatment, with success rates exceeding 95%. Boots-and-bar bracing for 4 years after correction is essential to prevent relapse.
Key Facts
- Definition: Congenital foot deformity with forefoot adduction, hindfoot varus and equinus
- Incidence: 1 per 1,000 live births (varies by ethnicity)
- Sex Ratio: Male:Female 2:1
- Laterality: Bilateral in 50% of cases
- Treatment:Ponseti method is gold standard (95%+ success rate)
- Key to Success: Brace compliance (boots-and-bar for 4 years)
Clinical Pearls
"CAVE" Mnemonic: The four deformity components in order of correction are: Cavus (high arch), Adductus (forefoot adducted), Varus (hindfoot inverted), Equinus (ankle plantarflexed). Correct CAVE in order — C-A-V first with casting, E last with tenotomy.
Tenotomy in 90%: Approximately 90% of clubfeet require percutaneous Achilles tenotomy after casting to correct the equinus. This is done in clinic under local anaesthesia and is definitive.
Relapse is Parent-Dependent: Relapse occurs in 40% if bracing is not used correctly. The single biggest predictor of relapse is brace non-compliance. Educate parents extensively.
Why This Matters Clinically
Clubfoot, if untreated, leads to permanent disability, painful walking on the outer edge of the foot, and difficulties with footwear. The Ponseti method has transformed outcomes — with appropriate treatment, children achieve normal functional feet. Early referral to a Ponseti-trained specialist is essential.
Incidence & Prevalence
- Incidence: 1 per 1,000 live births (worldwide average)
- Ethnic variation: Higher in Polynesian populations (6-7/1000), lower in East Asian populations (0.3-0.5/1000)
- UK incidence: Approximately 1,000 babies per year
- Trend: Stable incidence
Demographics
| Factor | Details |
|---|---|
| Sex | Male:Female 2:1 |
| Side | Right = Left = Bilateral (each ~33%) |
| Bilateral | 50% of cases |
| Family History | 25% have affected family member |
Risk Factors
Non-Modifiable:
- Male sex (2x risk)
- Family history (25% positive)
- Genetic syndromes (arthrogryposis, spina bifida)
- Oligohydramnios (theoretical — compression)
Modifiable:
| Risk Factor | Notes |
|---|---|
| Maternal smoking | Some evidence of increased risk |
| Amniocentesis <15 weeks | Associated with clubfoot |
Mechanism
Exact Aetiology Unknown — Multifactorial:
Theories:
- Germ plasm defect: Primary developmental abnormality of talus
- Neurogenic: Abnormal muscle innervation
- Vascular: Abnormal anterior tibial artery development
- Arrested development: Foot fails to derotate in utero
- Genetic: Polygenic inheritance pattern
Pathological Anatomy:
- Talus: Short neck, medially deviated
- Navicular: Displaced medially onto medial malleolus
- Calcaneus: Inverted, adducted, rotated medially
- Cuboid: Displaced medially
- Medial structures: Contracted (tibialis posterior, Achilles, ligaments)
Classification (CAVE Mnemonic)
| Component | Deformity | Anatomical Basis |
|---|---|---|
| Cavus | High longitudinal arch | First metatarsal plantarflexed |
| Adductus | Forefoot pointed inward | Tight medial structures |
| Varus | Heel turned inward | Calcaneus inverted under talus |
| Equinus | Foot plantarflexed | Short Achilles tendon |
Classification by Aetiology
| Type | Features | Prognosis |
|---|---|---|
| Idiopathic | Isolated clubfoot, otherwise normal child | Excellent with Ponseti |
| Neurogenic | Spina bifida, myelomeningocele | Variable; higher relapse |
| Syndromic | Arthrogryposis, chromosomal anomalies | Often resistant to treatment |
| Positional | Very flexible, correctable | Excellent; minimal treatment |
Symptoms
Prenatal:
At Birth:
Untreated (Historical):
Signs
Red Flags
[!CAUTION] Red Flags — Suggest complex or syndromic clubfoot:
- Associated spinal abnormality (sacral dimple, tuft of hair — spina bifida)
- Hip abnormality (DDH — occurs in 3-5% with clubfoot)
- Multiple joint contractures (arthrogryposis)
- Severe rigidity not responding to initial casting
- Neurological abnormality (check spine MRI)
Structured Approach
General:
- Full newborn examination (exclude syndromic features)
- Spine examination (sacral dimple, tuft of hair)
- Hip examination (Barlow/Ortolani for DDH)
- Both feet and legs examined
Specific Clubfoot Examination:
- Assess each CAVE component
- Test passibility of deformity (flexible vs rigid)
- Compare to contralateral side (if unilateral)
- Assess calf size (typically smaller on affected side)
Special Tests
| Test | Technique | Positive Finding | Significance |
|---|---|---|---|
| Pirani Score | 6-point scoring system | 0 = fully corrected; 6 = severe | Monitor progress of treatment |
| Dimeglio Score | Alternative severity score | Grade I-IV | Predict treatment difficulty |
| Passive Correction | Attempt to correct each component | Rigid = concerning | Syndromic clubfoot if very rigid |
| Hip Examination | Barlow and Ortolani | Instability | DDH association |
| Spine Examination | Inspect for dimple/tuft | Present | Possible spina bifida |
Pirani Scoring System
Hindfoot (3 points):
- Posterior crease severity (0-1)
- Emptiness of heel (0-1)
- Rigidity of equinus (0-1)
Midfoot (3 points):
- Medial crease severity (0-1)
- Lateral border curvature (0-1)
- Head of talus coverage (0-1)
Total: 0 (normal) to 6 (severe)
First-Line (Bedside)
- Clinical examination is diagnostic
- Pirani or Dimeglio scoring for severity and monitoring
- Hip examination for associated DDH
Laboratory Tests
| Test | Expected Finding | Purpose |
|---|---|---|
| Usually not required | — | Diagnosis is clinical |
| Karyotype | If syndromic features | Genetic diagnosis |
Imaging
| Modality | Findings | Indication |
|---|---|---|
| X-ray | Rarely needed for diagnosis | May assess talocalcaneal angle if needed |
| Ultrasound Hip | DDH screening | All babies with clubfoot |
| MRI Spine | Spinal dysraphism | If sacral dimple, neurological signs |
| Prenatal Ultrasound | Clubfoot visible at 18-20 weeks | Antenatal detection |
Diagnostic Criteria
Clinical diagnosis based on:
- Presence of CAVE deformity at birth
- Rigidity of deformity (cannot passively correct)
- Exclusion of positional talipes (which is flexible)
Management Algorithm
CLUBFOOT MANAGEMENT (PONSETI METHOD)
↓
┌─────────────────────────────────────────────────────┐
│ PHASE 1: CASTING │
│ │
│ • Weekly manipulation and above-knee casts │
│ • Correct CAVE in order: Cavus → Adductus → Varus │
│ • Do NOT correct equinus during casting │
│ • Typically 4-6 casts over 4-6 weeks │
│ • Monitor with Pirani score │
└─────────────────────────────────────────────────────┘
↓
┌─────────────────────────────────────────────────────┐
│ PHASE 2: ACHILLES TENOTOMY │
│ │
│ • Percutaneous tenotomy (90% of patients) │
│ • Done when CAV corrected but E persists │
│ • In clinic, local anaesthesia, small blade │
│ • Final cast for 3 weeks post-tenotomy │
│ • Tendon regenerates in lengthened position │
└─────────────────────────────────────────────────────┘
↓
┌─────────────────────────────────────────────────────┐
│ PHASE 3: BRACING (CRITICAL!) │
│ │
│ Boots-and-Bar (Foot Abduction Brace - FAB): │
│ • Full-time (23 hours/day) for 3 months │
│ • Then nights + naps until age 4 years │
│ • Set at 70° external rotation (affected side) │
│ │
│ ⚠ COMPLIANCE IS KEY — 40% relapse if non-compliant │
└─────────────────────────────────────────────────────┘
↓
RELAPSE?
↓
┌─────────────────────────────────────────────────────┐
│ Mild: Repeat casting series │
│ Equinus: Repeat Achilles tenotomy │
│ Dynamic supination (walking age): Tibialis anterior │
│ transfer (after age 2.5) │
│ Severe/Complex: Posteromedial release (rare now) │
└─────────────────────────────────────────────────────┘
Conservative Management (Ponseti Method)
Casting Phase:
- Begin as soon as possible (ideally within 1-2 weeks of birth)
- Weekly above-knee plaster casts
- Manipulation follows specific Ponseti technique
- Correct cavus first (supinate forefoot to align with hindfoot)
- Then correct adductus and varus by abducting foot with counter-pressure on lateral talar head (NEVER pronate)
- Do NOT attempt to correct equinus during casting — must be last
Achilles Tenotomy:
- Indicated when CAV corrected but foot cannot dorsiflex beyond neutral
- Done percutaneously in clinic or minor procedure room
- Local anaesthesia (EMLA cream + subcutaneous LA)
- Complete division of Achilles tendon
- Final above-knee cast for 3 weeks
- Tendon regenerates in lengthened position
Bracing Phase:
- Boots attached to bar at 70° external rotation (affected side), 40° (normal side)
- Bar width = shoulder width
- Full-time for first 3 months
- Then nights and naps until age 4 years
- Total duration: ~4 years
Surgical Management
Indications (Now Rare <5%):
- Failure of Ponseti method
- Severe rigid syndromic clubfoot
- Late-presenting neglected clubfoot
- Recurrent relapse despite proper bracing
Procedures:
| Procedure | Description | Indication |
|---|---|---|
| Tibialis Anterior Transfer | Transfer TAT to lateral cuneiform | Dynamic supination >2.5 years |
| Posteromedial Release | Extensive soft tissue release | Historically used; rarely now |
| External Fixation | Frame correction | Neglected/recurrent deformity |
| Osteotomies | Bony correction | Older child with rigid deformity |
Treatment-Related
| Complication | Cause | Prevention/Management |
|---|---|---|
| Cast sores | Pressure from cast | Proper casting technique, check after 24 hours |
| Cast slipping | Inadequate moulding | Above-knee cast essential |
| Rocker-bottom | Forced dorsiflexion too early | Never try to correct equinus before CAV |
| Bleeding post-tenotomy | Tenotomy complication | Pressure, elevation; rarely significant |
Relapse (Most Common Long-Term Issue)
- Incidence: 40% if non-compliant with bracing; <10% if compliant
- Risk factors: Non-compliance, syndromic clubfoot, severe initial deformity
- Management: Re-casting, repeat tenotomy, TAT transfer as needed
Late Complications
- Persistent calf atrophy: Common; usually not functionally significant
- Foot size difference: Affected foot usually 0.5-1 size smaller
- Residual deformity: May require late osteotomies
- Osteoarthritis: Rare if well-treated
Natural History
Untreated clubfoot leads to walking on the lateral border of the foot, painful calluses, difficulty with footwear, and significant disability. With proper Ponseti treatment, outcomes are excellent.
Outcomes with Treatment
| Variable | Outcome |
|---|---|
| Ponseti success rate | >95% functional correction |
| Tenotomy rate | 90% require tenotomy |
| Relapse with good compliance | 5-10% |
| Relapse with poor compliance | 40% |
| Long-term function | Near-normal gait and activity |
Prognostic Factors
Good Prognosis:
- Idiopathic clubfoot
- Early treatment
- Good brace compliance
- Supple deformity
Poor Prognosis:
- Syndromic or neurogenic clubfoot
- Delayed treatment
- Poor brace compliance
- Severe rigid deformity (high Pirani score)
Key Guidelines
-
Ponseti International Association — Provides training and standards for Ponseti method worldwide.
-
POSNA (Pediatric Orthopaedic Society of North America) — Endorses Ponseti method as gold standard.
Landmark Studies
Ponseti (1963-1996) — Original technique description
- Iowa long-term outcomes
- Key finding: Non-surgical correction possible in majority
- Clinical Impact: Revolutionised clubfoot treatment worldwide
Morcuende et al. (2004) — Compliance study
- Key finding: Relapse directly related to brace non-compliance
- Clinical Impact: Emphasised critical importance of parent education
Dobbs et al. (2004) — Long-term outcomes
- 30-year follow-up of Ponseti patients
- Key finding: Excellent functional outcomes maintained
- Clinical Impact: Confirmed durability of Ponseti correction
Evidence Strength
| Intervention | Level | Key Evidence |
|---|---|---|
| Ponseti method | 1a | Multiple cohort studies, meta-analyses |
| Achilles tenotomy | 2a | Large case series |
| Bracing (FAB) | 2a | Comparative studies showing relapse prevention |
| TAT for relapse | 2b | Case series |
What is Clubfoot?
Clubfoot is a condition where a baby is born with one or both feet turned inward and downward. The medical name is "talipes equinovarus" or "CTEV." It's one of the most common birth defects affecting bones and muscles, occurring in about 1 in every 1,000 babies.
Why does it matter?
Without treatment, clubfoot would make it very difficult to walk normally. Children would have to walk on the outside of their feet, causing pain and disability. The good news is that with proper treatment, children with clubfoot can have completely normal feet that work just like everyone else's.
How is it treated?
Treatment uses a method called the Ponseti method, which is very effective:
-
Casting (4-6 weeks): The foot is gently stretched into a better position, and a plaster cast is applied. This is done weekly, with each cast getting closer to the correct position.
-
Achilles tenotomy (9 out of 10 babies): A small cut is made to lengthen the tight tendon at the back of the ankle. This is done in clinic and isn't as scary as it sounds. A final cast is worn for 3 weeks after.
-
Boots-and-bar bracing (4 years): This is the most important part. Special boots attached to a bar are worn to keep the feet in the corrected position:
- Full-time for the first 3 months
- Then during sleep and naps until age 4
What to expect
- Treatment starts soon after birth
- Weekly clinic visits for 4-6 weeks
- Your child will have a small scar on the back of the ankle
- The affected foot and calf will always be slightly smaller — this is normal
- With proper brace wearing, your child should have a completely normal, functional foot
When to seek help
Contact your clinic if:
- The cast becomes loose or slips
- You see any skin marks or sores
- Your child seems in pain with the cast
- You're having trouble with the braces
- The foot seems to be turning back inward (relapse)
Primary Guidelines
- Ponseti International Association. Clubfoot: Ponseti Management. 3rd Edition. 2021.
Key Trials
-
Ponseti IV, Smoley EN. The classic: congenital club foot: the results of treatment. Clin Orthop Relat Res. 2009;467(5):1133-1145. PMID: 19219518
-
Morcuende JA, Dolan LA, Dietz FR, Ponseti IV. Radical reduction in the rate of extensive corrective surgery for clubfoot using the Ponseti method. Pediatrics. 2004;113(2):376-380. PMID: 14754952
-
Dobbs MB, Rudzki JR, Purcell DB, et al. Factors predictive of outcome after use of the Ponseti method for the treatment of idiopathic clubfeet. J Bone Joint Surg Am. 2004;86(1):22-27. PMID: 14711941
Further Resources
- Ponseti International Association: ponseti.info
- Steps Charity Worldwide (UK): steps-charity.org.uk
Medical Disclaimer: MedVellum content is for educational purposes and clinical reference. Clinical decisions should account for individual patient circumstances. Always consult appropriate guidelines and specialists for patient care.